Pulmonary arteriovenous fistula (PAVF) is abnormally dilated vessels that provide a right-to-left shunt between pulmonary artery and pulmonary vein and is clinically divided into iPhone 7/8/SE simple and complex type.Here, we report four cases of surgically resected sporadic PAVFs presenting various clinical and histologic spectrums.Cases 1 (a 57-old-female) and 2 (a 54-old-female) presented as incidentally identified single aneurysmal fistulas and the lesions were surgically removed without complication.
On the other hand, case 3 (an 11-old-male) showed diffuse dilated vascular sacs involving both lungs and caused severe hemodynamic Stoves STBI900G Built-In Double Gas Oven and pulmonary dysfunction.Embolization and surgical resection of the main lesion failed to relieve the symptoms.Case 4 (a 36-old-male) had a localized multiloculated cyst clinically mimicking congenital cystic adenomatoid malformation.
Microscopically, the lesion consisted of dilated thick vessels, consistent with the diagnosis of fistulous arteriovenous malformation/hemangioma.